Strokeisthesecondleadingcauseofdeathandmajorcauseoflong-termdisability,directlyimpactingthequalityoflife,worldwide.Strokeswithmorerare,andunknowncausesunfortunatelyreceivelittletonoattentionduetotheheterogeneityofdisordersandapoorunderstandingofclinicalfeatures.Thereareconsiderablevariationsintheetiologyofthisraresub-categoryofstroke;requiringheightenedclinicalawarenessforrecognition,evaluationandtreatment.Thisbookprovidesup-to-dateguidance,throughcasereportsconciselysummarisedbygloballeadersinthefielddescribingthediagnosisandtreatmentofrarecausesofstroke,fromvasculitis,hypercoagulablestates,hereditaryandgeneticfactors,cardioembolism,vasculopathies,venousocclusiveconditionstobonedisorders.Offeringpracticaladviceandalgorithms,thisbookaidstheclinicianinestablishinganaccuratediagnosisthroughdetailedevaluationofsuchpatients,leadingtoanearlydiagnosisimprovingriskassessmentandfamilycounselling.